• Users Online: 551
  • Print this page
  • Email this page
Year : 2019  |  Volume : 3  |  Issue : 3  |  Page : 180-182

Unicuspid Unicommissural Aortic Valve in Young Adult: Rare Congenital Abnormality Presenting as Symptomatic and Severe Aortic Stenosis

Department of Non Invasive Cardiology, Max Super Specialty Hospital, New Delhi, India

Correspondence Address:
Rahul Mehrotra
Max Super Speciality Hospital, 2, Press Enclave Road, Saket, New Delhi - 110 017
Login to access the Email id

Source of Support: None, Conflict of Interest: None

DOI: 10.4103/jiae.jiae_49_18

Rights and Permissions

Isolated aortic valve stenosis in adults with or without aortic regurgitation is almost always secondary to a congenital valvular malformation. These congenital malformations usually present as a bicuspid, quadricuspid, or unicuspid aortic valve. The unicuspid acommissural valve has no commissures or lateral attachments to the aorta at the level of the orifice and appears as a pinhole on imaging. The unicommissural UAV has one lateral commissural attachment to the aorta at the level of the orifice and appears as a slit-shaped structure. We report the case of a 21-year-old man who presented with dyspnea, palpitations and one episode of syncope on exertion. Transesophageal echocardiography confirmed a stenotic, unicuspid, unicommissural aortic valve with dilated ascending aorta. He underwent successful aortic valve replacement since the ascending aorta was only mildly dilated (40 mm). Postoperative course was uneventful and discharge from the hospital in stable condition.

Print this article     Email this article
 Next article
 Previous article
 Table of Contents

 Similar in PUBMED
   Search Pubmed for
   Search in Google Scholar for
 Related articles
 Citation Manager
 Access Statistics
 Reader Comments
 Email Alert *
 Add to My List *
 * Requires registration (Free)

 Article Access Statistics
    PDF Downloaded15    
    Comments [Add]    

Recommend this journal